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What is Fallot Pentalogy?

What is Fallot Pentalogy?

Pentalogy of Fallot is a term used to describe an association of Tetralogy of Fallot (TOF) with an atrial septal defect. 1. TOF is the most common form of cyanotic congenital heart disease and accounts for 5% to 10% of all congenital heart diseases (CHDs), with an incidence of 3 in 10000 live births.

What causes the tetralogy of Fallot?

Tetralogy of Fallot is a combination of four congenital heart defects. The four defects are a ventricular septal defect (VSD), pulmonary stenosis, a misplaced aorta and a thickened right ventricular wall (right ventricular hypertrophy). They usually result in a lack of oxygen-rich blood reaching the body.

Is tetralogy of Fallot a serious heart condition?

Because a baby with tetralogy of Fallot may need surgery or other procedures soon after birth, this birth defect is considered a critical congenital heart defect. Congenital means present at birth. This heart defect can cause oxygen in the blood that flows to the rest of the body to be reduced.

What is Coeur en Sabot?

Cœur en sabot (French for “clog-shaped heart”) is a radiological sign seen most commonly in patients with tetralogy of Fallot, a cyanotic congenital heart disease. It is a radiological term to describe the following findings in the x-ray: The cardiac size is normal or mildly enlarged.

What is the survival rate of tetralogy of Fallot?

Tetralogy of Fallot (ToF) is the most common type of cyanotic congenital heart disease. Since the first surgical repair in 1954, treatment has continuously improved. The treatment strategies currently used in the treatment of ToF result in excellent long-term survival (30 year survival ranges from 68.5% to 90.5%).

Can tetralogy of Fallot be cured?

There is no medical treatment for tetralogy of Fallot. The structural abnormalities in the heart require surgical correction. In most cases, infants undergo the operation within the first year of life.

How long do tetralogy of Fallot patients live?

Tetralogy of Fallot is a rather common complex cardiac malformation with an incidence of 0.1/1000 live births. Without surgical intervention, patients had a 1 year survival rate of 66%, 49% after 2 years and only 10–15% after more than 20 years [1,2].

How long can babies live with tetralogy of Fallot?

What is the life expectancy of someone with tetralogy of Fallot? It is difficult to predict how long a child with repaired Tetralogy of Fallot is going to live but data suggests that the outcome is generally good up to 30-40 years after complete repair.

What is the mortality rate of tetralogy of Fallot?

Survival of the 819 patients with repaired tetralogy of Fallot. The 10-, 20-, and 30-year survival rates were 95.8%, 92.7%, and 90.5%, respectively….Table 2.

Cause of Death No. (%)
Cardiovascular origin 15 (51.7)
Heart failure or pulmonary hypertension 7 (24.1)
Sudden cardiac death 5 (17.2)
Arrhythmia 3 (10.3)